Beckwith-wiedemann Syndrome with Cleft Palate
نویسندگان
چکیده
BECKWITH-WIEDEMANN SYNDROME WITH CLEFT PALATE (ABSTRACT): BeckwithWiedemann syndrome is a rare congenital disorder. Early diagnosis, proper counselling of parents is essential because of significant risk of subsequent development of malignant tumours, associated with this syndrome. Association of cleft palate in this syndrome is extremely rare. Specific difficulties and risks posed by the craniofacial abnormalities like macroglossia and cleft palate are highlighted and discussed along with the management options. The literature is reviewed and discussed.
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